ChaosKitty
Queen Bitch From Hell
Since these people were allowed to skate on millions of dollars worth of welfare fraud the first question is why the government is really allowing them to get away with the numerous crimes they are involved in including being so inbred and having so many children that this disease is an epidemic specifically in their community. Ont op of severe muscle damage where the born victims can't stand up on their own they are also so mentally retarded that they need livelong care. This is a tragedy that easily could be alleviated specifically because their founders both on the male and one of the female had these genes that created it. It is a bad situation that is getting worse.
http://www.reuters.com/article/us-usa-mormons-genes-idUSN0727298120070614
http://www.dailymail.co.uk/news/article-4740726/Extremely-rare-disease-common-FLDS-town.html
One-in-400million disability becomes COMMON in tiny polygamist Mormon town Hilldale where sufferers can't sit or stand without help after generations of inbreeding
Dr. Theodore Tarby, who specialized in rare childhood diseases, first discovered the problem in 1990, when a woman in the community brought her 10-year-old son to him.
The boy had unusual facial features, such as a prominent forehead, low-set ears, widely-spaced eyes and a small jaw. He was also severely physically and mentally disabled.
Dr. Tarby was stumped as to what condition the boy had until he sent a urine sample out for analysis.
That test came back position for fumarase deficiency, an extremely rare disorder that impacts the metabolism.
Fumarase deficiency happens when a person lacks the enzyme fumarase which helps drive energy to cells. It has the most severe impact on the brain, which takes up about 20 per cent of the body's energy.
Children who have it are missing parts of their brain, can't sit or stand without help, and often suffer from seizures. Their language skills are minimal and their IQ is usually around 25.
At that time, Dr. Tarby believed there were only 13 cases in the world, making the odds of having it about one in 400 million. But he soon discovered that his patient's sister, who was believed to suffer from cerebal palsy, also had the disease.
Dr. Tarby started working with the community after that and diagnosed eight more cases, in children ranging in age from 20 months to 12 years old.
All of the patients had the same facial characteristics, and most couldn't walk or even sit up.
Researchers found that the likelihood of having the disease was over one million times the global average.
The reason for this? Polygamy and the gradual inbreeding over generations.
The faulty gene traces back to one of the community's two founders Joseph Smith Jessop (seated, center right), and his first wife Martha Moore Yeates (seated center left). It's now estimated that 75 to 80 per cent of the community are related by blood to either Jessop or the other founder, John Y. Barlow * actually now both males that founded are proven to have had the gene along with one of thems wife[s']
The polygamist twin cities of Hilldale and Colorado City were founded in the 1930s by two men, John Y. Barlow and Joseph Smith Jessop.
The two men had become pariahs by the main Mormon church, which outlawed polygamy in 1904. They moved to Hilldale/Colorado City to set up their own community where they could continue to practice plural marriage.
The group was then, and is now, very insular. New people are not welcomed into the community, and in fact, young boys are often kicked out so that a select few men can have an excess of wives.
That means that the gene pool is small. In other words, most of the people who are in the community are related to each other.
'With polygymy you’re decreasing the overall genetic diversity because a few men are having a disproportionate impact on the next generation,' Mark Stoneking, a geneticist at the Max Planck Institute for Evolutionary Anthropology, in Germany, told the BBC. 'Random genetic mutations become more important.'
And that's a problem when it comes to recessive diseases like fumarase deficiency.
It's an exceptionally rare disease because it's recessive, meaning that in order to get it, both parents need to carry the gene.
The chances of that happening almost anywhere else in the world is extremely rare. But in the FLDS community in Hilldale and Colorado City, relatives marrying each other is a common occurrence.
It's said that 75 to 80 per cent of the population at the population in the community are blood related to one of the founders, either Barlow or Jessop.
http://www.reuters.com/article/us-usa-mormons-genes-idUSN0727298120070614
http://www.dailymail.co.uk/news/article-4740726/Extremely-rare-disease-common-FLDS-town.html
One-in-400million disability becomes COMMON in tiny polygamist Mormon town Hilldale where sufferers can't sit or stand without help after generations of inbreeding
- Fumarase deficiency, an extremely rare disease, has become increasingly common in the fundamentalist Mormon enclave on the Arizona-Utah border
- It causes severe mental and physical retardation
- Occurs in the towns of Hilldale and Colorado City on the Arizona-Utah border
- Town is infamous for being where FLDS head Warren Jeffs abused children
- The disease is recessive, which means that in order to get it, both parents must pass the gene on
- It's become a problem in the FLDS community, since many in the insular community are related to each other
- Occurrences of the disease are exploding too because the community practices polygamy, and men try to have as many children as they can with multiple wives
- Experts have warned the community against continued inbreeding, but they have refused to take the advice
Dr. Theodore Tarby, who specialized in rare childhood diseases, first discovered the problem in 1990, when a woman in the community brought her 10-year-old son to him.
The boy had unusual facial features, such as a prominent forehead, low-set ears, widely-spaced eyes and a small jaw. He was also severely physically and mentally disabled.
Dr. Tarby was stumped as to what condition the boy had until he sent a urine sample out for analysis.
That test came back position for fumarase deficiency, an extremely rare disorder that impacts the metabolism.
Fumarase deficiency happens when a person lacks the enzyme fumarase which helps drive energy to cells. It has the most severe impact on the brain, which takes up about 20 per cent of the body's energy.
Children who have it are missing parts of their brain, can't sit or stand without help, and often suffer from seizures. Their language skills are minimal and their IQ is usually around 25.
At that time, Dr. Tarby believed there were only 13 cases in the world, making the odds of having it about one in 400 million. But he soon discovered that his patient's sister, who was believed to suffer from cerebal palsy, also had the disease.
Dr. Tarby started working with the community after that and diagnosed eight more cases, in children ranging in age from 20 months to 12 years old.
All of the patients had the same facial characteristics, and most couldn't walk or even sit up.
Researchers found that the likelihood of having the disease was over one million times the global average.
The reason for this? Polygamy and the gradual inbreeding over generations.
The faulty gene traces back to one of the community's two founders Joseph Smith Jessop (seated, center right), and his first wife Martha Moore Yeates (seated center left). It's now estimated that 75 to 80 per cent of the community are related by blood to either Jessop or the other founder, John Y. Barlow * actually now both males that founded are proven to have had the gene along with one of thems wife[s']
The polygamist twin cities of Hilldale and Colorado City were founded in the 1930s by two men, John Y. Barlow and Joseph Smith Jessop.
The two men had become pariahs by the main Mormon church, which outlawed polygamy in 1904. They moved to Hilldale/Colorado City to set up their own community where they could continue to practice plural marriage.
The group was then, and is now, very insular. New people are not welcomed into the community, and in fact, young boys are often kicked out so that a select few men can have an excess of wives.
That means that the gene pool is small. In other words, most of the people who are in the community are related to each other.
'With polygymy you’re decreasing the overall genetic diversity because a few men are having a disproportionate impact on the next generation,' Mark Stoneking, a geneticist at the Max Planck Institute for Evolutionary Anthropology, in Germany, told the BBC. 'Random genetic mutations become more important.'
And that's a problem when it comes to recessive diseases like fumarase deficiency.
It's an exceptionally rare disease because it's recessive, meaning that in order to get it, both parents need to carry the gene.
The chances of that happening almost anywhere else in the world is extremely rare. But in the FLDS community in Hilldale and Colorado City, relatives marrying each other is a common occurrence.
It's said that 75 to 80 per cent of the population at the population in the community are blood related to one of the founders, either Barlow or Jessop.